von Hippel-Lindau syndrome (VHL) is a rare hereditary cancer syndrome associated with

• A specific type of kidney cancer called clear cell renal cell carcinoma
• Kidney cysts or pancreatic cysts
• Hemangioblastomas, or blood vessel tumors of the brain, spinal cord, and eye. Eye tumors are called retinal angiomas.
• A tumor of the adrenal gland called pheochromocytoma
• Noncancerous tumors near a man's testicles called epididymal cystadenomas
• Noncancerous tumors of the ear called endolymphatic sac tumors that may cause hearing loss